企业信息
第7年
- 入驻时间: 2015-11-06
- 联系人:顾磊
- 电话:021-60514606
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联系时,请说明易展网看到的
- Email:shybio@126.com
产品分类
产品详情
简单介绍:
Anti-Acid sphingomyelinase抗体供应商为您提供抗体的售前、售中、售后服务,现货供应,保证实验结果,无效可以免费退换,广泛应用于IHC、WB、 IF、IP、ELISA,质量保证,另外本公司生产经营各种单克隆抗体、多克隆抗体,标记二抗、**印迹常用试剂、**组化常用试剂,Anti-Acid sphingomyelinase抗体用于**组化实验,WB实验,相应的标记抗体有HRP标记抗体,FITC标记,BIO等。
详情介绍:
Rabbit Anti-Acid sphingomyelinase
Cat. Number:
YB6318R
Quantity size:
0.1ml
Concentration:
Anti-Acid sphingomyelinase抗体1mg/ml Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Converts sphingomyelin to ceramide. Also has phospholipase C activities toward 1,2-diacylglycerolphosphocholine and 1,2-diacylglycerolphosphoglycerol. Isoform 2 and isoform 3 have lost catalytic activity.
Involvement in disease: Defects in SMPD1 are the cause of Niemann-Pick disease type A (NPDA) ; also known as Niemann-Pick disease classical infantile form. It is an early-onset lysosomal storage disorder caused by failure to hydrolyze sphingomyelin to ceramide. It results in the accumulation of sphingomyelin and other metabolically related lipids in reticuloendothelial and other cell types throughout the body, leading to cell death. Anti-Acid sphingomyelinase抗体Niemann-Pick disease type A is a primarily neurodegenerative disorder characterized by onset within the first year of life, mental retardation, digestive disorders, failure to thrive, major hepatosplenomegaly, and severe neurologic symptoms. The severe neurological disorders and pulmonary infections lead to an early death, often around the age of four. Clinical features are variable. A phenotypic continuum exists between type A (basic neurovisceral) and type B (purely visceral) forms of Niemann-Pick disease, and the intermediate types encompass a cluster of variants combining clinical features of both types A and B.
Involvement in disease: Defects in SMPD1 are the cause of Niemann-Pick disease type A (NPDA) ; also known as Niemann-Pick disease classical infantile form. It is an early-onset lysosomal storage disorder caused by failure to hydrolyze sphingomyelin to ceramide. It results in the accumulation of sphingomyelin and other metabolically related lipids in reticuloendothelial and other cell types throughout the body, leading to cell death. Anti-Acid sphingomyelinase抗体Niemann-Pick disease type A is a primarily neurodegenerative disorder characterized by onset within the first year of life, mental retardation, digestive disorders, failure to thrive, major hepatosplenomegaly, and severe neurologic symptoms. The severe neurological disorders and pulmonary infections lead to an early death, often around the age of four. Clinical features are variable. A phenotypic continuum exists between type A (basic neurovisceral) and type B (purely visceral) forms of Niemann-Pick disease, and the intermediate types encompass a cluster of variants combining clinical features of both types A and B.
Also known as:
Anti-Acid sphingomyelinase抗体Acid sphingomyelinase; ASM; ASM_HUMAN; aSMase; NPD; Smpd1; Sphingomyelin phosphodiesterase 1 acid lysosomal; Sphingomyelin phosphodiesterase.
Specificity:
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Rabbit Polyclonal IgG, affinity purified by Protein A.
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Reacts with: Human,Anti-Acid sphingomyelinase抗体 Mouse, Rat, Dog, Pig, Cow, Rabbit, .
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Immunogen: KLH conjugated synthetic peptide derived from human Acid sphingomyelinase.
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Predicted Molecular Weight: 64kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
Anti-Acid sphingomyelinase抗体WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.yb650Mu01 主要碱性蛋白(MBP)多克隆抗体 Polyclonal Antibody to Major Basic Protein (MBP) Mus musculus (Mouse)
yb650Ra01 主要碱性蛋白(MBP)多克隆抗体 Polyclonal Antibody to Major Basic Protein (MBP) Rattus norvegicus (Rat)
yb650Po01 主要碱性蛋白(MBP)多克隆抗体 Polyclonal Antibody to Major Basic Protein (MBP) Sus scrofa; Porcine (Pig)
yb908Ge01 褪黑素(MT)多克隆抗体 Polyclonal Antibody to Melatonin (MT) General
yb575Hu01 胃动素(MTL)多克隆抗体 Polyclonal Antibody to Motilin (MTL) Homo sapiens (Human)
yb575Ra01 胃动素(MTL)多克隆抗体 Polyclonal Antibody to Motilin (MTL) Rattus norvegicus (Rat)
yb575Rb51 胃动素(MTL)多克隆抗体 Polyclonal Antibody to Motilin (MTL) Oryctolagus cuniculus (Rabbit)
yb575Bo01 胃动素(MTL)多克隆抗体 Polyclonal Antibody to Motilin (MTL) Bos taurus; Bovine (Cattle)
yb095Hu01 粘蛋白(MUC)多克隆抗体 Polyclonal Antibody to Mucin (MUC) Homo sapiens (Human)
yb095Po01 粘蛋白(MUC)多克隆抗体 Polyclonal Antibody to Mucin (MUC) Sus scrofa; Porcine (Pig)
yb480Ca01 肌红蛋白(MYO)多克隆抗体 Polyclonal Antibody to Myoglobin (MYO) Canis familiaris; Canine (Dog)
yb480Ga01 肌红蛋白(MYO)多克隆抗体 Polyclonal Antibody to Myoglobin (MYO) Chicken (Gallus)
yb098Hu01 肌浆球蛋白(Myo)多克隆抗体 Polyclonal Antibody to Myosin(Myo) Homo sapiens (Human)
yb098Rb51 肌浆球蛋白(Myo)多克隆抗体 Polyclonal Antibody to Myosin(Myo) Oryctolagus cuniculus (Rabbit)
yb218Ge01 **脱落酸(ABA)多克隆抗体 Polyclonal Antibody to Abscisic Acid (ABA) General
yb907Ge01 去甲肾上腺素(NE)多克隆抗体 Polyclonal Antibody to Noradrenaline (NE) General
yb121Ge01 **肽(OP)多克隆抗体 Polyclonal Antibody to Opioid Peptide (OP) General
yb115Pl01 多酚氧化酶(PPO)多克隆抗体
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.yb650Mu01 主要碱性蛋白(MBP)多克隆抗体 Polyclonal Antibody to Major Basic Protein (MBP) Mus musculus (Mouse)
yb650Ra01 主要碱性蛋白(MBP)多克隆抗体 Polyclonal Antibody to Major Basic Protein (MBP) Rattus norvegicus (Rat)
yb650Po01 主要碱性蛋白(MBP)多克隆抗体 Polyclonal Antibody to Major Basic Protein (MBP) Sus scrofa; Porcine (Pig)
yb908Ge01 褪黑素(MT)多克隆抗体 Polyclonal Antibody to Melatonin (MT) General
yb575Hu01 胃动素(MTL)多克隆抗体 Polyclonal Antibody to Motilin (MTL) Homo sapiens (Human)
yb575Ra01 胃动素(MTL)多克隆抗体 Polyclonal Antibody to Motilin (MTL) Rattus norvegicus (Rat)
yb575Rb51 胃动素(MTL)多克隆抗体 Polyclonal Antibody to Motilin (MTL) Oryctolagus cuniculus (Rabbit)
yb575Bo01 胃动素(MTL)多克隆抗体 Polyclonal Antibody to Motilin (MTL) Bos taurus; Bovine (Cattle)
yb095Hu01 粘蛋白(MUC)多克隆抗体 Polyclonal Antibody to Mucin (MUC) Homo sapiens (Human)
yb095Po01 粘蛋白(MUC)多克隆抗体 Polyclonal Antibody to Mucin (MUC) Sus scrofa; Porcine (Pig)
yb480Ca01 肌红蛋白(MYO)多克隆抗体 Polyclonal Antibody to Myoglobin (MYO) Canis familiaris; Canine (Dog)
yb480Ga01 肌红蛋白(MYO)多克隆抗体 Polyclonal Antibody to Myoglobin (MYO) Chicken (Gallus)
yb098Hu01 肌浆球蛋白(Myo)多克隆抗体 Polyclonal Antibody to Myosin(Myo) Homo sapiens (Human)
yb098Rb51 肌浆球蛋白(Myo)多克隆抗体 Polyclonal Antibody to Myosin(Myo) Oryctolagus cuniculus (Rabbit)
yb218Ge01 **脱落酸(ABA)多克隆抗体 Polyclonal Antibody to Abscisic Acid (ABA) General
yb907Ge01 去甲肾上腺素(NE)多克隆抗体 Polyclonal Antibody to Noradrenaline (NE) General
yb121Ge01 **肽(OP)多克隆抗体 Polyclonal Antibody to Opioid Peptide (OP) General
yb115Pl01 多酚氧化酶(PPO)多克隆抗体