产品详情
  • 产品名称:Anti-ALAD抗体

  • 产品型号:δ氨基乙酰丙酸脱水酶抗体
  • 产品厂商:科研抗体
  • 产品价格:0
  • 折扣价格:0
  • 产品文档:
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简单介绍:
Anti-ALAD抗体供应商为您提供抗体的售前、售中、售后服务,现货供应,保证实验结果,无效可以免费退换,广泛应用于IHC、WB、 IF、IP、ELISA,质量保证,另外本公司生产经营各种单克隆抗体、多克隆抗体,标记二抗、**印迹常用试剂、**组化常用试剂,Anti-ALAD抗体用于**组化实验,WB实验,相应的标记抗体有HRP标记抗体,FITC标记,BIO等。
详情介绍:
Rabbit  Anti-ALAD
Cat. Number:
YB7954R
Quantity size:
0.1ml
Concentration:
Anti-ALAD抗体1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Catalyzes an early step in the biosynthesis of tetrapyrroles. Binds two molecules of 5-aminolevulinate per subunit, each at a distinct site, and catalyzes their condensation to form porphobilinogen. Involvement in disease:Defects in ALAD are the cause of acute hepatic porphyria (AHP). AHP is a form of porphyria. Anti-ALAD抗体Porphyrias are inherited defects in the biosynthesis of heme, resulting in the accumulation and increased excretion of porphyrins or porphyrin precursors. They are classified as erythropoietic or hepatic, depending on whether the enzyme deficiency occurs in red blood cells or in the liver. AHP is characterized by attacks of gastrointestinal disturbances, abdominal colic, paralysis, and peripheral neuropathy. Most attacks are precipitated by drugs, alcohol, caloric deprivation, infections, or endocrine factors.
Also known as:
Anti-ALAD抗体ALAD; ALADH; ALADR; Aminolevulinate dehydratase; Aminolevulinate, delta, dehydratase; Delta aminolevulinic acid dehydratase; Delta-aminolevulinic acid dehydratase; HEM2_HUMAN; Lv; PBGS; Porphobilinogen synthase.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Cow, Horse, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human ALAD.
Predicted Molecular Weight: 36kDa.
Storage:
Shipped at 4℃, Anti-ALAD抗体Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
Anti-ALAD抗体WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.yb120Hu01 干细胞因子(SCF)多克隆抗体 Polyclonal Antibody to Stem Cell Factor (SCF) Homo sapiens (Human)
yb120Mu01 干细胞因子(SCF)多克隆抗体 Polyclonal Antibody to Stem Cell Factor (SCF) Mus musculus (Mouse)
yb120Ra01 干细胞因子(SCF)多克隆抗体 Polyclonal Antibody to Stem Cell Factor (SCF) Rattus norvegicus (Rat)
yb121Hu01 干细胞因子受体(SCFR)多克隆抗体 Polyclonal Antibody to Stem Cell Factor Receptor (SCFR) Homo sapiens (Human)
yb121Mu01 干细胞因子受体(SCFR)多克隆抗体 Polyclonal Antibody to Stem Cell Factor Receptor (SCFR) Mus musculus (Mouse)
yb122Fi01 基质细胞衍生因子1(SDF1)多克隆抗体 Polyclonal Antibody to Stromal Cell Derived Factor 1 (SDF1) Danio rerio (Zebrafish)
yb122Hu01 基质细胞衍生因子1(SDF1)多克隆抗体 Polyclonal Antibody to Stromal Cell Derived Factor 1 (SDF1) Homo sapiens (Human)
yb122Mu01 基质细胞衍生因子1(SDF1)多克隆抗体 Polyclonal Antibody to Stromal Cell Derived Factor 1 (SDF1) Mus musculus (Mouse)
yb122Ra01 基质细胞衍生因子1(SDF1)多克隆抗体 Polyclonal Antibody to Stromal Cell Derived Factor 1 (SDF1) Rattus norvegicus (Rat)
yb123Cp01 转化生长因子α(TGFα)多克隆抗体 Polyclonal Antibody to Transforming Growth Factor Alpha (TGFa) Capra hircus; Caprine (Goat)
yb123Po01 转化生长因子α(TGFα)多克隆抗体 Polyclonal Antibody to Transforming Growth Factor Alpha (TGFa) Sus scrofa; Porcine (Pig)
yb123Rb51 转化生长因子α(TGFα)多克隆抗体 Polyclonal Antibody to Transforming Growth Factor Alpha (TGFa) Oryctolagus cuniculus (Rabbit)
yb123Si01 转化生长因子α(TGFα)多克隆抗体 Polyclonal Antibody to Transforming Growth Factor Alpha (TGFa) Rhesus monkey (Simian)
yb124Fi01 转化生长因子β1(TGFβ1)多克隆抗体 Polyclonal Antibody to Transforming Growth Factor Beta 1 (TGFb1) Danio rerio (Zebrafish)
yb124Si01 转化生长因子β1(TGFβ1)多克隆抗体 Polyclonal Antibody to Transforming Growth Factor Beta 1 (TGFb1) Rhesus monkey (Simian)
yb125Bo01 **球蛋白样EGF样域酪氨酸激酶1(Tie1)多克隆抗体 Polyclonal Antibody to Tyrosine Kinase With Immunoglobulin Like And EGF Like Domains Protein 1 (Tie1) Bos taurus; Bovine (Cattle)
yb125Fi01 **球蛋白样EGF样域酪氨酸激酶1(Tie1)多克隆抗体
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