苏氨酸tRNA连接酶2抗体
规格：1mg/1ml
英文名： TARS2
别名： FLJ12528; mitochondrial; SYTM_HUMAN; TARS 2; Tars2; TARSL1; Threonine tRNA ligase 2; threonine tRNA ligase 2, mitochondrial; Threonine tRNA ligase; Threonine--tRNA ligase; threonine--tRNA ligase, mito
分子量： 81kDa
储存液：0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glyce
克隆类型：Polyclonal
亚型：IgG
纯化方法：affinity purified by Protein A
**原：KLH conjugated synthetic peptide derived from human TARS2
交叉反应：Human, Mouse, Rat, Cow,
细胞定位：
苏氨酸tRNA连接酶2抗体产品介绍：Function: Catalytic activityi; ATP + L-threonine + tRNA(Thr) = AMP + diphosphate + L-threonyl-tRNA(Thr). Subcellular Location: Mitochondrion matrix. DISEASE: The disease is caused by mutations affecting the gene represented in this entry. Disease description:A mitochondrial disorder characterized by a lethal encephalomyopathy. Shortly苏氨酸tRNA连接酶2抗体 after birth, affected individuals manifest axial hypotonia, limb hypertonia, psychomotor delay, and increased serum lactate. Additional features include subsarcolemmal lipofuscin-positive deposits in muscle, cerebral spongiosis, and hepatic steatosis. Similarity: Belongs to the class-II aminoacyl-tRNA synthetase family. Database links: Entrez Gene: 80222 Human Entrez Gene: 71807 Mouse Entrez Gene: 310672苏氨酸tRNA连接酶2抗体 Rat Omim: 612805 Human SwissProt: Q9BW92 Human SwissProt: Q3UQ84 Mouse SwissProt: Q68FW7 Rat Unigene: 288974 Human Unigene: 271754 Mouse Unigene: 44110 Rat Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
苏氨酸tRNA连接酶2抗体产品应用：WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500 （石蜡切片需做抗原修复） not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user.
研究领域：细胞生物 转录调节因子 表观遗传学
储存条件： Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
来源： Rabbit
外观： Lyophilized or Liquid